Pemphigus erythematosus
Pemphigus Erythematosus
Pemphigus Erythematosus (pronunciation: pem-FI-gus eri-the-MAT-o-sus) is a rare, chronic autoimmune disease that primarily affects the skin. It is a variant of Pemphigus Foliaceus and is also known as Senear-Usher syndrome.
Etymology
The term 'Pemphigus' is derived from the Greek word 'pemphix', meaning 'bubble' or 'blister'. 'Erythematosus' is derived from the Greek word 'erythema', which means 'redness'. The disease is named for its characteristic presentation of blistering and redness of the skin.
Symptoms
The primary symptom of Pemphigus Erythematosus is the formation of blisters or erosions on the skin, particularly in areas exposed to sunlight such as the face and chest. These blisters often become crusted and may be accompanied by redness and scaling. Other symptoms may include itching, pain, and general discomfort.
Causes
Pemphigus Erythematosus is an autoimmune disease, which means it is caused by the body's immune system mistakenly attacking healthy cells. In this case, the immune system targets desmogleins, which are proteins that help cells in the skin stick together. This results in the formation of blisters and erosions.
Diagnosis
Diagnosis of Pemphigus Erythematosus typically involves a physical examination, a review of the patient's medical history, and specific diagnostic tests. These tests may include a skin biopsy, where a small sample of skin is removed and examined under a microscope, and blood tests to detect antibodies associated with the disease.
Treatment
Treatment for Pemphigus Erythematosus primarily involves managing symptoms and preventing complications. This may include the use of topical or systemic corticosteroids, immunosuppressive drugs, and other therapies to reduce inflammation and control the immune response.
Related Terms
External links
- Medical encyclopedia article on Pemphigus erythematosus
- Wikipedia's article - Pemphigus erythematosus
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