Schilder's disease
Schilder's Disease
Schilder's Disease (pronounced: SHIL-ders disease), also known as Myelinoclastic Diffuse Sclerosis, is a rare, progressive, and degenerative neurological condition that primarily affects children and young adults.
Etymology
The disease is named after the German psychiatrist Paul Ferdinand Schilder, who first described the condition in 1912. The term "myelinoclastic" refers to the destruction of the myelin sheath, a protective layer that covers nerve cells.
Definition
Schilder's Disease is characterized by the gradual deterioration of the central nervous system, specifically the brain and spinal cord. It is a form of Multiple Sclerosis (MS), but it is distinguished by its more severe and rapid progression.
Symptoms
Symptoms of Schilder's Disease can vary widely among individuals but often include cognitive impairment, motor skill difficulties, behavioral problems, and seizures.
Diagnosis
Diagnosis of Schilder's Disease is often challenging due to its rarity and the similarity of its symptoms to other neurological disorders. It is typically confirmed through magnetic resonance imaging (MRI) showing two or more large lesions in the brain.
Treatment
There is currently no cure for Schilder's Disease. Treatment is symptomatic and supportive, often involving a combination of physical therapy, occupational therapy, and medication to manage symptoms.
Prognosis
The prognosis for individuals with Schilder's Disease is generally poor, with most experiencing a progressive decline in physical and cognitive abilities. However, the rate of progression can vary significantly among individuals.
See Also
External links
- Medical encyclopedia article on Schilder's disease
- Wikipedia's article - Schilder's disease
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