Idiopathic Pulmonary Fibrosis

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Idiopathic Pulmonary Fibrosis (IPA: /ˌɪdiəˈpæθɪk pʊlˈmɒnəri ˈfaɪbrəsɪs/) is a chronic, progressive lung disease that results in scarring (fibrosis) of the lungs. The term "idiopathic" is derived from the Greek words idios (own, personal) and pathos (suffering), and it means the cause of the condition is unknown.

Definition

Idiopathic Pulmonary Fibrosis (IPF) is a specific form of chronic, progressive fibrosing interstitial pneumonia of unknown cause, primarily occurring in older adults, limited to the lungs, and associated with the histopathologic and/or radiologic pattern of usual interstitial pneumonia (UIP).

Symptoms

Common symptoms of IPF include shortness of breath, a persistent dry cough, fatigue, unexplained weight loss, and aching muscles and joints. It is important to note that the presence and severity of symptoms can vary greatly from person to person.

Diagnosis

Diagnosis of IPF involves a variety of tests, including pulmonary function tests, high-resolution computed tomography (HRCT), and sometimes a lung biopsy.

Treatment

While there is currently no cure for IPF, treatments are available that can help slow the progression of the disease and improve quality of life. These include antifibrotic drugs such as Pirfenidone and Nintedanib, as well as supportive treatments like oxygen therapy and pulmonary rehabilitation.

Prognosis

The prognosis for IPF can vary greatly from person to person. Some people may live with the disease for many years, while others may experience a more rapid progression of symptoms.

Epidemiology

IPF is a rare disease, affecting approximately 13-20 per 100,000 people worldwide each year. It is more common in men than in women, and most often affects people over the age of 50.

See also

External links

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