Rasmussen syndrome
Rasmussen Syndrome
Rasmussen Syndrome (pronounced rahs-MOO-sen sin-drome), also known as Rasmussen's Encephalitis, is a rare, progressive neurological disorder, primarily affecting one hemisphere of the brain. It is named after the Danish neurologist, Theodore Rasmussen, who first described the condition in the 1950s.
Etymology
The term "Rasmussen Syndrome" is derived from the name of the neurologist, Theodore Rasmussen, who first identified and described the condition. The term "syndrome" is derived from the Greek word "syndromē", which means "concurrence of symptoms, concourse of people".
Definition
Rasmussen Syndrome is characterized by frequent and severe seizures, loss of motor skills and speech, paralysis on one side of the body (hemiparesis), inflammation of the brain (encephalitis), and mental deterioration. It most often affects children between the ages of 2 and 10.
Symptoms
The initial symptoms of Rasmussen Syndrome may include seizures that are not responsive to treatment (refractory epilepsy), and loss of motor skills and speech. As the disease progresses, symptoms may include weakness or paralysis on one side of the body, mental deterioration, and inflammation of the brain.
Diagnosis
Diagnosis of Rasmussen Syndrome is typically based on the characteristic symptoms, a detailed patient history, a thorough clinical evaluation, and a variety of specialized tests such as Magnetic Resonance Imaging (MRI) and Electroencephalogram (EEG).
Treatment
Treatment for Rasmussen Syndrome is symptomatic and supportive. Medications may be used to help control seizures. In some cases, a surgical procedure known as a hemispherectomy, in which one cerebral hemisphere is removed or disconnected, may be necessary.
Related Terms
External links
- Medical encyclopedia article on Rasmussen syndrome
- Wikipedia's article - Rasmussen syndrome
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