Evans syndrome

Evans Syndrome

Evans syndrome (pronounced: /ˈiːvənz ˈsɪndroʊm/) is a rare autoimmune disorder in which the immune system destroys the body's red blood cells, platelets, and sometimes neutrophils. This condition is named after Dr. Robert S. Evans, who first described it in 1951.

Etymology

The term "Evans syndrome" is derived from the name of Dr. Robert S. Evans, an American physician who first described the condition in a medical journal in 1951. The word "syndrome" comes from the Greek "σύνδρομον" (syndromon), meaning "concurrence of symptoms," or "running together."

Definition

Evans syndrome is characterized by the simultaneous or sequential development of autoimmune hemolytic anemia (AIHA) and immune thrombocytopenia (ITP). In some cases, the condition may also involve neutropenia, a decrease in the number of neutrophils, a type of white blood cell.

Symptoms

Symptoms of Evans syndrome may include fatigue, shortness of breath, rapid heart rate, pale skin, frequent or severe infections, easy bruising or bleeding, and petechiae (small red spots under the skin caused by bleeding).

Diagnosis

Diagnosis of Evans syndrome is based on clinical findings, a complete blood count, and other specialized blood tests. The presence of both AIHA and ITP in a patient is a strong indicator of Evans syndrome.

Treatment

Treatment for Evans syndrome typically involves medications to suppress the immune system, such as corticosteroids, rituximab, and sometimes splenectomy (surgical removal of the spleen).

Related Terms

External links

Medical encyclopedia article on Evans syndrome
Wikipedia's article - Evans syndrome

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